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Erdheim–Chester disease

Erdheim–Chester disease

Image Modality: 
clinical photo
Benign/Malignant: 
Benign
Body Region: 
pelvis - entire
Bone Name: 
ilium

Erdheim–Chester disease (ECD)

Image Modality: 
Xray
Benign/Malignant: 
Benign
Body Region: 
pelvis - entire
Bone Name: 
ilium
Tumor Behavior: 
latent

Erdheim–Chester disease (ECD)

Image Modality: 
Xray
Benign/Malignant: 
Benign
Body Region: 
pelvis - entire
Bone Name: 
ilium
Tumor Behavior: 
latent

Erdheim–Chester disease (ECD)

Erdheim–Chester disease (also known as Erdheim–Chester syndrome or polyostotic sclerosing histiocytosis) is a rare disease characterized by the abnormal multiplication of a specific type of white blood cells called histiocytes, or tissue macrophages (technically, this disease is termed a non-Langerhans-cell histiocytosis). Usually, onset is in middle age. The disease involves an infiltration of lipid-laden macrophages, multinucleated giant cells, an inflammatory infiltrate of lymphocytes and histiocytes in the bone marrow, and a generalized sclerosis of the long bones
ECD affects predominantly adults, with a mean age of 53 years



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